Title: Extraocular Muscles: Extraocular Muscle Involvement in Disease☆
Abstract: The extraocular muscles (EOMs) have unique functional and structural properties that truly set them apart from the other skeletal muscles in the body. Their most outstanding feature is a distinct behavior in disease. The EOMs remain unaffected in Duchenne muscular dystrophy and merosin deficient congenital muscle dystrophy, two devastating muscle diseases causing severe handicap and precocious death. The EOMs are remarkably spared in motor neuron disease such as amyotrophic lateral sclerosis, also a lethal neuromuscular disease. In contrast, these muscles are selectively affected in Miller Fisher syndrome, and they are often the primary target in myasthenia gravis, two diseases affecting the neuromuscular junction.
Publication Year: 2016
Publication Date: 2016-11-21
Language: en
Type: book-chapter
Indexed In: ['crossref']
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