An Adult Case of Fulminant Wilson's Disease

Name: Work Video:
Duration: 3 min 30 s
Satoru Yatsuji; Katsutoshi TOKUSHIGE; Etsuko Hashimoto; Masakazu Yamamoto; Ken TAKASAKI; Takashi Someya; Hiromitsu Kumada; Keiko SHIRATORI
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'https://openalex.org/W145137507'], 'abstract_inverted_index': {'症例は25歳女性.': [0], '肝機能障害を指摘された既往はない.': [1], '原因不明の劇症肝炎を発症し当院紹介受診となった.': [2], '血漿交換を繰り返すも検査所見,': [3], '肝性脳症の改善なく,': [4], '生体肝移植を施行した.': [5], '術後,': [6], '肝組織銅含有量より原疾患はWilson病であると診断した.': [7], '我々の検索しえた限り,': [8], '25歳の本例は劇症肝炎で発症したWilson病としては本邦最高齢であり,': [9], '成人の原因不明の劇症肝炎でもWilson病は鑑別診断として考えるべき疾患と考えられた.': [10], 'また,': [11], '劇症肝炎を起こすWilson病では,': [12], 'ALP/T-bil比,': [13], 'AST/ALT比が他の原因による劇症肝炎との鑑別に有効であり,': [14], 'さらに尿中銅,': [15], '肝組織銅含有量により確定診断に至るものと考えられた.': [16], '現在では,': [17], '遺伝子検査によってWilson病の診断が可能であり,': [18], '本症例でも現在検査中である.': [19]}, 'cited_by_api_url': 'https://api.openalex.org/works?filter=cites:W1996755079', 'counts_by_year': [{'year': 2020, 'cited_by_count': 1}], 'updated_date': '2024-12-11T01:53:47.999693', 'created_date': '2016-06-24'}
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