Title: Polyostotic Fibrous Dysplasia With Cutaneous Pigmentation
Abstract: <h3>Introduction</h3> FIBROUS dysplasia may be manifested by involvement of only one bone (monostotic), more than one (polyostotic), or by McCune-Albright syndrome. The original descriptions of McCune-Albright syndrome in this country consisted of café au lait spots, polyostotic fibrous dysplasia, and sexual precocity.<sup>1-3</sup>There are a number of good reviews describing the clinical, radiological, and pathological aspects of this syndrome to which the reader is referred.<sup>1-8</sup>In order to make this diagnosis, the classical triad should be present although some investigators<sup>5,6</sup>do not consider sexual precocity to be necessary. Lichtenstein,<sup>9</sup>in 1938 and again in 1942 in collaboration with Jaffe,<sup>10</sup>stressed the pathological aspects of the bony abnormalities of the disease and termed the true nature of these as a fibrous dysplasia. A 6-year-old Negro boy was admitted to the Pediatric Service of the Boston City Hospital, presenting with polyostotic fibrous dysplasia and café au lait
Publication Year: 1965
Publication Date: 1965-06-01
Language: en
Type: article
Indexed In: ['crossref', 'pubmed']
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Cited By Count: 3
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