Abstract: Pseudotumor cerebri or idiopathic intracranial hypertension is a rare condition in children most commonly presenting with headache and vomiting, without any cause identified. Here we report a case of 5year old boy with chronic headache with incidental finding of pseudotumor cerebri without any complications on acetazolamide on follow up. Pseudotumor cerebri is a rare condition but with a morbidity of visual loss and cranial nerve palsy. Hence early diagnosis and management is necessary.